ea0029p54 | Adrenal cortex | ICEECE2012
Reisch N.
, Willige M.
, Kohn D.
, Schwarz H.
, Allolio B.
, Reincke M.
, Quinkler M.
, Hahner S.
, Beuschlein F.
Background: Adrenal crisis (AC) is a life-threatening complication in patients with congenital adrenal hyperplasia due to classical 21-hydroxylase deficiency (21-OHD). AC was defined as an acute state of health impairment which required i.v. glucocorticoid administration and hospital admission. No data on AC over life-time in 21-OHD is available.Study design: In a retrospective study AC was studied following two approaches: a) questionnaire-based: 122 ad...